Hemifacial Microsomia Surgical Approach and Anotia Reconstruction: A Case Report.

In vivo (Athens, Greece) 2024 Vol.38(5) p. 2550-2556

Bini A, Derka S, Stavrianos S

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Abstract

[BACKGROUND/AIM] Hemifacial microsomia (HFM) is the second most common congenital anomaly of the craniomaxillofacial region after the cleft lip and palate. This malformation is characterized by unilateral mandible and ear hypoplasia. Treatment varies and depends on different phenotypes. Severe deficiencies require multiple reconstructive surgeries to address facial asymmetries. This study aimed to review the surgical approach and evaluate the postoperative results of a case with right hemifacial microsomia and anotia.

[CASE REPORT] This is the case of a 35-year-old female patient who, after multiple graft operations in the right mandible due to hemifacial microsomia, was operated for auricle reconstruction. Initially, a three-dimensional custom made Medpor (porex) was used, covered by the superficial temporal fascia. Subsequently, due to inflammation and partial exposure of this porous polyethylene implant (PPI), a temporalis muscular flap along with the deep temporal fascia were used as a salvage operation. Ten months later, the patient underwent deep plane face lift combined with open rhinoplasty. Lefort I osteotomies and transoral lip lengthening through a transection of the levator nasi septi muscle were also performed. Ear helix reconstruction was completed with a rotation scalp flap after tissue expansion. The patient had an uncomplicated postoperative course with an aesthetically acceptable result.

[CONCLUSION] As a congenital disorder, hemifacial microsomia is present at birth and successful reconstruction is of fundamental importance for the smooth integration of these individuals into society. The multiple asymmetries, the affected topographic area of the face, as well as the onset in neonatal age constitute a challenge for reconstructive surgery.

추출된 의학 개체 (NER)

유형영어 표현한국어 / 풀이UMLS CUI출처등장
시술 flap 피판재건술 dict 2
해부 mandible 하악골 dict 2
시술 rhinoplasty 코성형술 dict 1
시술 face lift 안면거상술 dict 1
해부 palate scispacy 1
해부 ear scispacy 1
해부 graft scispacy 1
해부 auricle scispacy 1
해부 temporalis muscular flap scispacy 1
해부 levator scispacy 1
해부 septi muscle scispacy 1
해부 tissue scispacy 1
해부 smooth scispacy 1
합병증 superficial temporal scispacy 1
합병증 scalp flap scispacy 1
약물 HFM → Hemifacial microsomia C0265240
Goldenhar Syndrome
scispacy 1
약물 polyethylene C0032487
polyethylenes
scispacy 1
기법 open rhinoplasty 개방형 접근법 dict 1
질환 Hemifacial Microsomia C0265240
Goldenhar Syndrome
scispacy 1
질환 congenital anomaly C0000768
Congenital Abnormality
scispacy 1
질환 cleft lip C0008924
Cleft upper lip
scispacy 1
질환 palate C0700374
Palate
scispacy 1
질환 malformation C0000768
Congenital Abnormality
scispacy 1
질환 right hemifacial microsomia C0265240
Goldenhar Syndrome
scispacy 1
질환 anotia C0702139
Congenital absence of external ear
scispacy 1
질환 inflammation C0021368
Inflammation
scispacy 1
질환 temporalis muscular flap scispacy 1
질환 congenital disorder C0242354
Congenital Disorders
scispacy 1
질환 HFM → Hemifacial microsomia scispacy 1
질환 lip scispacy 1
기타 patient scispacy 1

MeSH Terms

Humans; Female; Adult; Plastic Surgery Procedures; Goldenhar Syndrome; Treatment Outcome; Facial Asymmetry; Surgical Flaps

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