[Sigmoid neovagina: apropos of 2 cases].
Abstract
The presence of ambiguous external genitals can be related with a number of nosologic entities. We can find the female form with hypertrophic clitoris and vaginal hypoplasia in a wide variety of phenotype presentations. We have two young girls with ambiguous external genitals, where we notice hypertrophic clitoris and vaginal hypoplasia, with the diagnosis of mixed gonadal dysgenesis and androgen insensitivity syndrome (Morri's Syndrome). They have been operated several times: gonadectomy, genitoplasty, vaginoplasty and mammoplasty. We have made a neovagina, using a segment of sigma and preserving the walls of the former vagina. The surgical technique we used, consisted in the abdominoperineal descent of the segment of sigmoid colon and anastomosis with the back wall of the former vagina and the perineum; after that, we split the intervaginal septum, linking these two structures and reaching a lonely introitus vaginae. The hormonal treatment for the girl with mixed gonadal dysgenesis with estrogen and progestogen induces normal menstruations; we only use estrogen for the patient with Morri's Syndrome. The histology showed that there were dysgenetic gonads in one of the patients and testicular tissue without gonadal elements. Both girls have had a good evolution, with no problems and an excellent aesthetic and functional result.
추출된 의학 개체 (NER)
| 유형 | 영어 표현 | 한국어 / 풀이 | UMLS CUI | 출처 | 등장 |
|---|---|---|---|---|---|
| 시술 | mammoplasty
|
유방성형술 | dict | 1 | |
| 해부 | genitals
|
scispacy | 1 | ||
| 해부 | vaginal
|
scispacy | 1 | ||
| 해부 | gonadal
|
scispacy | 1 | ||
| 해부 | gonads
|
scispacy | 1 | ||
| 해부 | testicular tissue
|
scispacy | 1 | ||
| 해부 | septum
|
비중격 | dict | 1 | |
| 합병증 | Sigmoid neovagina
|
scispacy | 1 | ||
| 합병증 | vaginal hypoplasia
|
scispacy | 1 | ||
| 합병증 | genitoplasty
|
scispacy | 1 | ||
| 합병증 | perineum
|
scispacy | 1 | ||
| 합병증 | introitus
|
scispacy | 1 | ||
| 약물 | estrogen
|
C0014939
estrogens
|
scispacy | 1 | |
| 약물 | progestogen
|
C0033306
Progestins
|
scispacy | 1 | |
| 질환 | ambiguous external genitals
|
C0266362
Ambiguous Genitalia
|
scispacy | 1 | |
| 질환 | hypertrophic clitoris
|
C0156394
Hypertrophy of clitoris
|
scispacy | 1 | |
| 질환 | vaginal hypoplasia
|
C0345309
Hypoplasia of vagina
|
scispacy | 1 | |
| 질환 | dysgenesis
|
C0000768
Congenital Abnormality
|
scispacy | 1 | |
| 질환 | androgen insensitivity syndrome
|
C0039585
Androgen-Insensitivity Syndrome
|
scispacy | 1 | |
| 질환 | genitoplasty
|
scispacy | 1 | ||
| 질환 | gonadal dysgenesis
|
C0018051
Gonadal Dysgenesis
|
scispacy | 1 | |
| 질환 | sigmoid colon
|
scispacy | 1 | ||
| 기타 | female
|
scispacy | 1 | ||
| 기타 | vagina
|
scispacy | 1 | ||
| 기타 | girl
|
scispacy | 1 |
MeSH Terms
Adolescent; Androgen-Insensitivity Syndrome; Colon, Sigmoid; Estrogen Replacement Therapy; Female; Follow-Up Studies; Gonadal Dysgenesis, Mixed; Hormone Replacement Therapy; Humans; Male; Progestins; Time Factors; Vagina
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