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[Sigmoid neovagina: apropos of 2 cases].

Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia Pediatrica 1999 Vol.12(2) p. 83-7

Sánchez-Martín R, Molina E, Cerdá J, Navascués JA, Barrientos G, Romero R, Vázquez J

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Abstract

The presence of ambiguous external genitals can be related with a number of nosologic entities. We can find the female form with hypertrophic clitoris and vaginal hypoplasia in a wide variety of phenotype presentations. We have two young girls with ambiguous external genitals, where we notice hypertrophic clitoris and vaginal hypoplasia, with the diagnosis of mixed gonadal dysgenesis and androgen insensitivity syndrome (Morri's Syndrome). They have been operated several times: gonadectomy, genitoplasty, vaginoplasty and mammoplasty. We have made a neovagina, using a segment of sigma and preserving the walls of the former vagina. The surgical technique we used, consisted in the abdominoperineal descent of the segment of sigmoid colon and anastomosis with the back wall of the former vagina and the perineum; after that, we split the intervaginal septum, linking these two structures and reaching a lonely introitus vaginae. The hormonal treatment for the girl with mixed gonadal dysgenesis with estrogen and progestogen induces normal menstruations; we only use estrogen for the patient with Morri's Syndrome. The histology showed that there were dysgenetic gonads in one of the patients and testicular tissue without gonadal elements. Both girls have had a good evolution, with no problems and an excellent aesthetic and functional result.

추출된 의학 개체 (NER)

유형영어 표현한국어 / 풀이UMLS CUI출처등장
시술 mammoplasty 유방성형술 dict 1
해부 genitals scispacy 1
해부 vaginal scispacy 1
해부 gonadal scispacy 1
해부 gonads scispacy 1
해부 testicular tissue scispacy 1
해부 septum 비중격 dict 1
합병증 Sigmoid neovagina scispacy 1
합병증 vaginal hypoplasia scispacy 1
합병증 genitoplasty scispacy 1
합병증 perineum scispacy 1
합병증 introitus scispacy 1
약물 estrogen C0014939
estrogens
scispacy 1
약물 progestogen C0033306
Progestins
scispacy 1
질환 ambiguous external genitals C0266362
Ambiguous Genitalia
scispacy 1
질환 hypertrophic clitoris C0156394
Hypertrophy of clitoris
scispacy 1
질환 vaginal hypoplasia C0345309
Hypoplasia of vagina
scispacy 1
질환 dysgenesis C0000768
Congenital Abnormality
scispacy 1
질환 androgen insensitivity syndrome C0039585
Androgen-Insensitivity Syndrome
scispacy 1
질환 genitoplasty scispacy 1
질환 gonadal dysgenesis C0018051
Gonadal Dysgenesis
scispacy 1
질환 sigmoid colon scispacy 1
기타 female scispacy 1
기타 vagina scispacy 1
기타 girl scispacy 1

MeSH Terms

Adolescent; Androgen-Insensitivity Syndrome; Colon, Sigmoid; Estrogen Replacement Therapy; Female; Follow-Up Studies; Gonadal Dysgenesis, Mixed; Hormone Replacement Therapy; Humans; Male; Progestins; Time Factors; Vagina

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