Congenital cutis laxa: a case report and review of loose skin syndromes.

Annals of plastic surgery 1993 Vol.30(3) p. 252-6

Thomas WO, Moses MH, Craver RD, Galen WK

Abstract

Congenital cutis laxa is a deforming disease that may present for plastic surgical consultation during childhood. Failure to differentiate cutis laxa, with near normal wound healing, from the other forms of hyperelasticity syndromes with poor wound healing, has historically led to conflicting recommendations regarding the surgical management of patients presenting with loose skin. A face-lift and direct nasolabial fold excision was performed in a 10-year old patient with congenital cutis laxa with a good result. The other major syndromes presenting with loose skin as a clinical feature are reviewed and distinguished from cutis laxa. Plastic surgical procedures can be aesthetically and psychologically beneficial in children with congenital cutis laxa, and can be recommended without overt fear of wound disruption, poor scarring, and medical catastrophies that can occur with other hyperelasticity syndromes.

추출된 의학 개체 (NER)

유형영어 표현한국어 / 풀이UMLS CUI출처등장
해부 skin scispacy 1
합병증 wound scispacy 1
합병증 nasolabial scispacy 1
합병증 cutis laxa scispacy 1
질환 Congenital cutis laxa scispacy 1
질환 loose skin syndromes scispacy 1
질환 cutis laxa C0010495
Cutis Laxa
scispacy 1
질환 hyperelasticity C3280023
Hyperelasticity
scispacy 1
질환 disease scispacy 1
기타 patients scispacy 1
기타 patient scispacy 1
기타 children scispacy 1

MeSH Terms

Child; Cutis Laxa; Female; Follow-Up Studies; Humans; Rhytidoplasty; Skin